ISSN 2756-3324
African Journal of Medicine and Surgery ISSN 2756-3324 Vol. 9 (4), pp. 001-004, April, 2022. Available online at www.internationalscholarsjournals.org © International Scholars Journals
Full Length Research Paper
Uncommon Presentation of Factor XIII Deficiency: Two Cases of Spontaneous Splenic Rupture in Young Patients
Kakil Ibrahim Rasul*, Mohamed Sadiq Ahmed and Abdul-Rahman Zar Gul
Hamad Medical Corporation, Al-Amal Hospital, P.O. Box 3050, Doha, Qatar.
Accepted 23 September, 2021
Abstract
Factor XIII deficiency is a rare bleeding disorder, and spontaneous spleen rapture is not reported in cases of this disorder. We report 2 cases of spontaneous ruptured spleen in 2 young Pakistani boys who were known factor XIII deficiency who were presented at the same time within 24 h. Both cases were recovered and one was successfully treated conservatively while the other treated surgically by spleenectomy. It should also remind physicians that bleeding disorders may have unusual presentations and should keep in mind ruptured spleen in the differential diagnosis of patient with factor XIII deficiency presenting with acute abdomen. The treatment is either surgery or conservatively depending on the progress of the bleeding.
Key words: Factor XIII deficiency, ruptured spleen, bleeding diathesis.